
Patient Education Leaflet
Interstitial Lung Disease and Pulmonary Fibrosis: A RespCAIR Patient Guide
ILD includes a wide range of conditions that affect the lung tissue between the air sacs (the interstitium). Some forms are related to autoimmune conditions, environmental or occupational exposures, or medications. Idiopathic pulmonary fibrosis (IPF) is one specific type. Specialist assessment combines clinical, imaging and lung function information to reach an accurate diagnosis.
Common symptoms
- Progressive breathlessness on exertion
- Persistent dry cough
- Fatigue
- Finger clubbing in some forms
- Sometimes joint pain or rash when linked to autoimmune disease
When to seek specialist review
- Unexplained breathlessness lasting more than a few weeks
- Persistent dry cough with normal initial investigations
- Abnormal chest imaging suggesting ILD
- Family history of pulmonary fibrosis
- Connective tissue or autoimmune disease with chest symptoms
